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Linear Nevus Sebaceous Syndrome in a Child With Ocular Choristoma and Hemimegalencephaly

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Date
2011-09-01
Author
ULUSAL, Hande Arda
Su, Ozlem
Onsun, NAHİDE
OZKAYA, Dilek Biyik
Advisor
Type
Article
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Abstract
Linear nevus sebaceous syndrome (LNSS) is a phakomatosis, associated with a variety of developmental abnormalities of ocular, nervous, skeletal, cardiovascular and urogenital systems. In LNSS, choristomas and colobomas are frequently seen signs, but complex choristomas are rare. We describe a case of a 3-year-old boy with a yellow alopecic plaque on his scalp, face and neck as well as a mass in the episcleral region since birth. He also had epileptic seizures since one year old. Histopathological examination of episcleral specimen revealed choristoma. Magnetic resonance imaging of the brain identified hemimegalencephaly, hemicerebral atrophy, and lateral ventricular enlargement (Turkderm 2011; 45: 155-7)
Subject
Su O., ULUSAL H. A. , OZKAYA D. B. , Onsun N., -Linear Nevus Sebaceous Syndrome in a Child With Ocular Choristoma and Hemimegalencephaly-, TURKDERM-ARCHIVES OF THE TURKISH DERMATOLOGY AND VENEROLOGY, cilt.45, ss.155-157, 2011
URI
https://hdl.handle.net/20.500.12645/4081
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  • Tıp Fakültesi [2546]
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  • Yayınlar - Eserler [9983]

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BEZMIALEM VAKIF UNIVERSITY

About us |Policies | Library | Contact us | Send Feedback | Sitemap | Admin

Bezmialem Vakıf Üniversitesi, Adnan Menderes Bulvarı Vatan Caddesi 34093 Fatih, İstanbul / TURKEY
Copyright © Bezmialem Vakıf Üniversitesi

Creative Commons Lisansı
Bezmialem Institutional Repository, Creative Commons Alıntı-GayriTicari-Türetilemez 4.0 Uluslararası Lisansı ile lisanslanmıştır.

OpenAccess@BVU

Support by  UNIREPOS