Publication: Idiopathic Systemic Capillary Leak Syndrome: A Case Report
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Date
2016-02-01
Authors
Authors
YARDIMCI, Bulent
Kazancioglu, RÜMEYZA
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Abstract
Introduction: Idiopathic systemic capillary leak syndrome (ISCLS) is rarely seen, and presents with recurrent episodes of hypotension,
shock, hemoconcentration, and hypoproteinemia. The main pathology is the dysfunction of the vascular endothelium, and it is
characterized by an increase of capillary permeability that is accompanied by the loss of intravascular fluid and protein.
Case Presentation: We present a 58-year-old female who presented with peripheral edema, leg pain, and syncope at the emergency
department. Interestingly demyemilising neuropathy, which is a rare finding, ensued on day 4. She is still being treated using intravenous
immunoglobulin therapy.
Conclusions: The early signs and symptoms of ISCLS may be subtle; therefore the diagnosis can easily be missed and prompt
treatment of the syndrome may be postponed. Thus, the clinician must consider ISCLS in differential diagnosis in cases of hypotension,
hemoconcentration, and hypoalbuminemia.
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Citation
YARDIMCI B., Kazancioglu R., -Idiopathic Systemic Capillary Leak Syndrome: A Case Report-, IRANIAN RED CRESCENT MEDICAL JOURNAL, cilt.18, 2016